Targeted Therapies

Formerly BioOncology Watch

www.tgt-therapies.com

june 2004

FARNESYL TRANSFERASE INHIBITION

Tipifarnib. Three studies of the novel farnesyl transferase inhibitor (FTI) tipifarnib were recently reported in the literature. FTIs are targeted therapies that modulate tumor signaling cascades by inhibition of the enzyme, farnesyl transferase. Farnesylation is critical to the activation of several oncoproteins, including Ras proteins that are the products of mutant ras genes. In the first study Razelle Kurzrock and colleagues enrolled 28 patients with intermediate-1- to high-risk myelodysplastic syndromes (MDS) into a study of oral tipifarnib (R115777) 600 mg bid given for 4 weeks every 6 weeks. Two patients achieved a complete remission (bone marrow with < 5% blasts and resolution of dysplasia; peripheral blood with no abnormal cells and granulocytes > 109/L and platelets > 100 x 109/L for ≥ 4 weeks; and resolution of pre-existing splenomegaly) and 1 patient had a partial remission. The durations of the complete remissions (CRs) were 4 and 11 months and the partial remission (PR) lasted for 2 months. None of the responders had ras mutations. Eleven patients (41%) developed tipifarnib-related toxicity necessitating dose reduction in 4 patients and discontinuation of therapy in 7 patients within the first 12 weeks of treatment. Dose reductions to 300 mg bid were well tolerated. In a second study, Melissa Alsina et al treated 43 consecutive patients with previously treated and progressive multiple myeloma with tipifarnib 600 mg bid for 3 weeks every 4 weeks. The treatment was found to suppress farnesyltransferase activity in bone marrow and peripheral blood mononuclear cells and to inhibit HDJ-2 protein farnesylation in mononuclear and myeloma cells. Sixty-four percent of patients had disease stabilization, but no patients showed a complete or partial response. The most common toxicity was fatigue; other adverse events included diarrhea, nausea, neuropathy, anemia, and thrombocytopenia. In addition, Eric Van Cutsem et al conducted a double-blind, phase III study in which 688 patients with advanced pancreatic adenocarcinoma were randomized to receive tipifarnib plus gemcitabine or placebo plus gemcitabine. No differences in overall or progression-free survival times were noted between treatment groups. However, combination therapy was tolerated with acceptable toxicity. These studies demonstrated that: oral tipifarnib can inhibit farnesylation clinically and has modest activity against MDS; MDS patients did not tolerate 600 mg bid of tipifarnib; and combining tipifarnib with standard cytotoxic chemotherapy is feasible for solid tumor patients. However, in multiple myeloma, despite its apparent inhibition of farnesylation, no clinical responses were noted in the trial. (Kurzrock R, et al. J Clin Oncol 2004;22:1287-1292; Alsina M, et al. Blood 2004;103:3271-3277; Van Cutsem E, et al. J Clin Oncol 2004;22:1430-1438)

 

MONOCLONAL ANTIBODIES

Cetuximab in refractory colorectal cancer. Cetuximab is a monoclonal antibody directed against the ligand-binding site of the epidermal growth factor receptor (EGFR). When bound to EGFR, cetuximab blocks the activation of EGFR tyrosine kinase by EGF or TGF-a, thereby inhibiting the growth of tumors overexpressing EGFR. A phase II study demonstrated that the combination of cetuximab plus irinotecan achieved a 22.5% response rate in a population of 120 colorectal cancer patients in clinical failure while on prior irinotecan therapy. These findings led Leonard Saltz and associates to conduct a phase II study in which 57 patients with EGFR-positive colorectal cancer who had previously received irinotecan-based treatments and experienced clinical failure were given weekly infusions of single-agent cetuximab (first dose was 400 mg/m2 infused over 2 hours followed by subsequent weekly treatments of 250 mg/m2 infused over 1 hour). Five patients (9%) achieved a PR and 21 patients had minor responses or stable disease. The median survival time was 6.4 months. The most common adverse events were an acne-like rash (86%) and a composite of asthenia, fatigue, malaise, and lethargy (56%). Three patients experienced grade 3 allergic reactions. This study showed that single-agent cetuximab has modest activity and is well tolerated in patients with refractory colorectal cancer. Further studies of cetuximab in combination with standard therapies are warranted. (Saltz LB, et al. J Clin Oncol 2004;22:1201-1208)

 

Alemtuzumab. Gerard Lozanski and others report the results of 36 consecutive patients with fludarabine-refractory chronic lymphocytic leukemia (CLL) treated with alemtuzumab, an anti-CD52 monoclonal antibody (Vysis Incorporated). Alemtuzumab was administered by a stepped-up dosing schedule (3 mg Day 1, 10 mg Day 2, and 30 mg Day 3 intravenously (i.v.), followed by 30 mg three times weekly for a total of 12 weeks of treatment). Two patients (6%) attained a CR and 9 patients (25%) had a PR. The median duration of response was 10 months (range, 3-36 months). In addition, a subpopulation of 15 patients with p53 mutations or deletions [del17 (p13.1)] were identified. Patients with p53 mutations or deletions have a poor prognosis and are known to be refractory to chlorambucil, fludarabine, and rituximab treatments. Alemtuzumab treatment resulted in clinical responses in 6 (40%) of these 15 patients with a median response duration of 8 months (range, 3-17 months). These data suggest that alemtuzumab may be effective therapy for patients with CLL associated with p53 mutations or deletions. In a second study Gunilla Enblad and coworkers treated 14 patients with refractory peripheral T-cell lymphoma (PTL) with alemtuzumab therapy for 12 weeks using the rapidly escalating dose schedule described previously. These patients have an extremely poor prognosis when disease progression develops after or during conventional chemotherapy. During this pilot study of alemtuzumab treatment, 3 patients achieved a CR and 2 patients had a PR (overall response rate of 36%). Cytomegalovirus reactivation occurred in 6 patients, pulmonary aspergillosis in 2 patients, and pancytopenia in 4 patients. EBV-related hemophagocytosis was seen in 2 patients and 5 patients died due to treatment-related causes. These preliminary findings suggested that alemtuzumab has activity in patients with advanced PTL; however it is associated with significant toxicity. Further investigation is warranted in patients with less advanced disease. (Lozanski G, et al. Blood 2004;103:3278-3281; Enblad G, et al. Blood 2004;103:2920-2924)

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